Annotation Detail

Information
Associated Genes
FGFR3
Associated Variants
FGFR3 p.Ter809Cysext*? (p.*809Cext*?) ( ENST00000340107.9, ENST00000352904.6, ENST00000412135.7, ENST00000440486.8, ENST00000481110.7 )
FGFR3 p.Ter809Cysext*? (p.*809Cext*?) ( ENST00000340107.9, ENST00000352904.6, ENST00000412135.7, ENST00000440486.8, ENST00000481110.7 )
Associated Disease
Thanatophoric dysplasia type 1
Source Database
ClinVar
Description
NM_000142.5(FGFR3):c.2421A>C (p.Ter807Cys) AND Thanatophoric dysplasia type 1
ClinVar Allele ID
76471
ClinVar RefSeq Alternation Syntax
NM_000142.5:c.2421A>C
ClinVar RefSeq Alternation Syntax
NM_001163213.2:c.2427A>C
ClinVar RefSeq Alternation Syntax
NM_001354809.2:c.2424A>C
ClinVar RefSeq Alternation Syntax
NM_001354810.2:c.2353A>C
ClinVar RefSeq Alternation Syntax
NR_148971.2:n.2847A>C
ClinVar RefSeq Alternation Syntax
NM_022965.4:c.2085A>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-05-08
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000055765
ClinVar Disease
Thanatophoric dysplasia type 1
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs