Annotation Detail

Information
Associated Genes
ACTA2
Associated Variants
ACTA2 p.Met49Val (p.M49V) ( ENST00000713602.1, ENST00000371927.7, ENST00000713598.1, ENST00000458159.6, ENST00000713599.1, ENST00000713600.1, ENST00000713597.1, ENST00000224784.10, ENST00000415557.2, ENST00000713601.1 )
ACTA2 p.Met49Val (p.M49V) ( ENST00000224784.10, ENST00000415557.2, ENST00000458159.6, ENST00000713597.1, ENST00000713598.1, ENST00000713599.1, ENST00000713600.1, ENST00000713601.1, ENST00000713602.1, ENST00000371927.7 )
Associated Disease
Aortic aneurysm, familial thoracic 6
Source Database
ClinVar
Description
NM_001613.4(ACTA2):c.145A>G (p.Met49Val) AND Aortic aneurysm, familial thoracic 6
ClinVar Allele ID
76367
ClinVar RefSeq Alternation Syntax
NM_001141945.3:c.145A>G
ClinVar RefSeq Alternation Syntax
NM_001406462.1:c.145A>G
ClinVar RefSeq Alternation Syntax
NM_001406471.1:c.145A>G
ClinVar RefSeq Alternation Syntax
NM_001406466.1:c.145A>G
ClinVar RefSeq Alternation Syntax
NM_001406463.1:c.145A>G
ClinVar RefSeq Alternation Syntax
NM_001406464.1:c.145A>G
ClinVar RefSeq Alternation Syntax
NM_001320855.2:c.145A>G
ClinVar RefSeq Alternation Syntax
NM_001613.4:c.145A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2011-05-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000055648
ClinVar Disease
Aortic aneurysm, familial thoracic 6
Observed Origin Sample
germline
Pubmed
21248741
Drugs