Annotation Detail

Information
Associated Genes
AIRE
Associated Variants
AIRE p.Cys311Tyr (p.C311Y) ( ENST00000291582.6 )
AIRE p.Cys311Tyr (p.C311Y) ( ENST00000291582.6 )
Associated Disease
Polyglandular autoimmune syndrome, type 1
Source Database
ClinVar
Description
NM_000383.4(AIRE):c.932G>A (p.Cys311Tyr) AND Polyglandular autoimmune syndrome, type 1
ClinVar Allele ID
70862
ClinVar RefSeq Alternation Syntax
NM_000383.4:c.932G>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000049634
ClinVar Disease
Polyglandular autoimmune syndrome, type 1
Observed Origin Sample
not provided
Drugs