Annotation Detail

Information
Associated Genes
LAMA4
Associated Variants
LAMA4 p.Arg1080Ter (p.R1080*) ( ENST00000230538.12, ENST00000389463.9, ENST00000424408.6, ENST00000522006.5 )
LAMA4 p.Arg1080Ter (p.R1080*) ( ENST00000230538.12, ENST00000389463.9, ENST00000424408.6, ENST00000522006.5 )
Associated Disease
dilated cardiomyopathy 1JJ
Source Database
ClinVar
Description
NM_001105206.3(LAMA4):c.3238C>T (p.Arg1080Ter) AND Dilated cardiomyopathy 1JJ
ClinVar Allele ID
59492
ClinVar RefSeq Alternation Syntax
NM_001105206.3:c.3238C>T
ClinVar RefSeq Alternation Syntax
NM_001105207.3:c.3217C>T
ClinVar RefSeq Alternation Syntax
NM_002290.5:c.3217C>T
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2023-01-23
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000043518
ClinVar Disease
Dilated cardiomyopathy 1JJ
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
17646580
Drugs