Annotation Detail

Information
Associated Genes
TSC2
Associated Variants
TSC2 p.Phe1645CysfsTer7 (p.F1645Cfs*7) ( ENST00000642936.1, ENST00000219476.9, ENST00000645186.2, ENST00000643088.1, ENST00000401874.7, ENST00000642561.1, ENST00000644329.1, ENST00000568454.6, ENST00000644335.1, ENST00000642206.2, ENST00000643946.1, ENST00000439673.6, ENST00000642365.2, ENST00000646388.1, ENST00000642797.1, ENST00000350773.9, ENST00000382538.10, ENST00000644043.1 )
TSC2 p.Phe1645CysfsTer7 (p.F1645Cfs*7) ( ENST00000219476.9, ENST00000350773.9, ENST00000382538.10, ENST00000401874.7, ENST00000439673.6, ENST00000568454.6, ENST00000642206.2, ENST00000642365.2, ENST00000642561.1, ENST00000642797.1, ENST00000642936.1, ENST00000643088.1, ENST00000643946.1, ENST00000644043.1, ENST00000644329.1, ENST00000644335.1, ENST00000645186.2, ENST00000646388.1 )
Associated Disease
Tuberous sclerosis syndrome
Source Database
ClinVar
Description
NM_000548.5(TSC2):c.4934_4935del (p.Phe1645fs) AND Tuberous sclerosis syndrome
ClinVar Allele ID
59143
ClinVar RefSeq Alternation Syntax
NM_001363528.2:c.4736_4737del
ClinVar RefSeq Alternation Syntax
NM_001318832.2:c.4766_4767del
ClinVar RefSeq Alternation Syntax
NM_001370405.1:c.4805_4806del
ClinVar RefSeq Alternation Syntax
NM_001318829.2:c.4589_4590del
ClinVar RefSeq Alternation Syntax
NM_001318831.2:c.4202_4203del
ClinVar RefSeq Alternation Syntax
NM_001114382.3:c.4865_4866del
ClinVar RefSeq Alternation Syntax
NM_001318827.2:c.4625_4626del
ClinVar RefSeq Alternation Syntax
NM_001077183.3:c.4733_4734del
ClinVar RefSeq Alternation Syntax
NM_021055.3:c.4805_4806del
ClinVar RefSeq Alternation Syntax
NM_001370404.1:c.4802_4803del
ClinVar RefSeq Alternation Syntax
NM_000548.5:c.4934_4935del
Clinical Significance Description
not provided
Clinical Significance Review Status
no assertion provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000043248
ClinVar Disease
Tuberous sclerosis syndrome
Observed Origin Sample
germline
Drugs