Annotation Detail

Information
Associated Genes
EYA1
Associated Variants
EYA1 p.Leu403PhefsTer6 (p.L403Ffs*6) ( ENST00000303824.11, ENST00000340726.8, ENST00000388741.7, ENST00000419131.6, ENST00000388742.8, ENST00000388740.4, ENST00000388743.6, ENST00000643681.1, ENST00000644229.1, ENST00000644712.1, ENST00000645793.1, ENST00000647540.1 )
EYA1 p.Leu403PhefsTer6 (p.L403Ffs*6) ( ENST00000303824.11, ENST00000340726.8, ENST00000388740.4, ENST00000388741.7, ENST00000388742.8, ENST00000388743.6, ENST00000419131.6, ENST00000643681.1, ENST00000644229.1, ENST00000644712.1, ENST00000645793.1, ENST00000647540.1 )
Associated Disease
Rare genetic deafness
Source Database
ClinVar
Description
NM_000503.6(EYA1):c.1122del (p.Leu374fs) AND Rare genetic deafness
ClinVar Allele ID
57263
ClinVar RefSeq Alternation Syntax
NM_001370333.1:c.1209del
ClinVar RefSeq Alternation Syntax
NM_172059.5:c.1122+25119del
ClinVar RefSeq Alternation Syntax
NM_001288575.2:c.756del
ClinVar RefSeq Alternation Syntax
NM_001370335.1:c.1122del
ClinVar RefSeq Alternation Syntax
NM_001370336.1:c.1119+25119del
ClinVar RefSeq Alternation Syntax
NM_000503.6:c.1122del
ClinVar RefSeq Alternation Syntax
NM_172058.4:c.1122del
ClinVar RefSeq Alternation Syntax
NM_001288574.2:c.1104del
ClinVar RefSeq Alternation Syntax
NM_001370334.1:c.1122del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2011-02-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000041385
ClinVar Disease
Rare genetic deafness
Observed Origin Sample
germline
Drugs