Annotation Detail

Information
Associated Genes
BRAF
Associated Variants
BRAF p.Glu541Gln (p.E541Q) ( ENST00000288602.11, ENST00000496384.7, ENST00000644969.2, ENST00000646891.2 )
BRAF p.Glu541Gln (p.E541Q) ( ENST00000288602.11, ENST00000496384.7, ENST00000644969.2, ENST00000646891.2 )
Associated Disease
Cardio-facio-cutaneous syndrome
Source Database
ClinVar
Description
NM_004333.6(BRAF):c.1501G>C (p.Glu501Gln) AND Cardio-facio-cutaneous syndrome
ClinVar Allele ID
53974
ClinVar RefSeq Alternation Syntax
NM_001374258.1:c.1621G>C
ClinVar RefSeq Alternation Syntax
NM_001378469.1:c.1435G>C
ClinVar RefSeq Alternation Syntax
NM_004333.6:c.1501G>C
ClinVar RefSeq Alternation Syntax
NM_001378474.1:c.1501G>C
ClinVar RefSeq Alternation Syntax
NM_001378472.1:c.1345G>C
ClinVar RefSeq Alternation Syntax
NM_001378475.1:c.1237G>C
ClinVar RefSeq Alternation Syntax
NM_001378470.1:c.1399G>C
ClinVar RefSeq Alternation Syntax
NM_001378467.1:c.1510G>C
ClinVar RefSeq Alternation Syntax
NM_001378473.1:c.1345G>C
ClinVar RefSeq Alternation Syntax
NM_001354609.2:c.1501G>C
ClinVar RefSeq Alternation Syntax
NM_001374244.1:c.1621G>C
ClinVar RefSeq Alternation Syntax
NM_001378468.1:c.1501G>C
ClinVar RefSeq Alternation Syntax
NM_001378471.1:c.1390G>C
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2010-04-23
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000037923
ClinVar Disease
Cardio-facio-cutaneous syndrome
Observed Origin Sample
germline
Drugs