Annotation Detail

Information
Associated Genes
TPM1
Associated Variants
TPM1 p.Met8Arg (p.M8R) ( ENST00000560970.6, ENST00000714017.1, ENST00000267996.11, ENST00000559556.5, ENST00000358278.7, ENST00000561266.6, ENST00000403994.9, ENST00000288398.10, ENST00000610733.1, ENST00000357980.9, ENST00000714014.1, ENST00000559397.6, ENST00000714013.1 )
TPM1 p.Met8Arg (p.M8R) ( ENST00000267996.11, ENST00000288398.10, ENST00000357980.9, ENST00000358278.7, ENST00000403994.9, ENST00000559397.6, ENST00000559556.5, ENST00000560970.6, ENST00000561266.6, ENST00000610733.1, ENST00000714013.1, ENST00000714014.1, ENST00000714017.1 )
Associated Disease
Primary dilated cardiomyopathy
Source Database
ClinVar
Description
NM_001018005.2(TPM1):c.23T>G (p.Met8Arg) AND Primary dilated cardiomyopathy
ClinVar Allele ID
52576
ClinVar RefSeq Alternation Syntax
NM_001018005.2:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_001018006.2:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_001018020.2:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_001365777.1:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_001301244.2:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_001018007.2:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_001365778.1:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_000366.6:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_001365779.1:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_001365776.1:c.23T>G
ClinVar RefSeq Alternation Syntax
NM_001018004.2:c.23T>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2008-03-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000036318
ClinVar Disease
Primary dilated cardiomyopathy
Observed Origin Sample
germline
Drugs