Annotation Detail

Information
Associated Genes
MYO7A
Associated Variants
MYO7A p.Gly2187Asp (p.G2187D) ( ENST00000409709.9, ENST00000409619.6, ENST00000458637.6 )
MYO7A p.Gly2187Asp (p.G2187D) ( ENST00000409619.6, ENST00000409709.9, ENST00000458637.6 )
Associated Disease
Usher syndrome
Source Database
ClinVar
Description
NM_000260.4(MYO7A):c.6560G>A (p.Gly2187Asp) AND Usher syndrome
ClinVar Allele ID
52505
ClinVar RefSeq Alternation Syntax
NM_001127180.2:c.6440G>A
ClinVar RefSeq Alternation Syntax
NM_000260.4:c.6560G>A
ClinVar RefSeq Alternation Syntax
NM_001369365.1:c.6413G>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2022-08-03
Clinical Significance Review Status
reviewed by expert panel
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000036241
ClinVar Disease
Usher syndrome
Observed Origin Sample
germline
Drugs