Annotation Detail

Information
Associated Genes
MYBPC3
Associated Variants
MYBPC3 p.Glu542Gln (p.E542Q) ( ENST00000545968.6, ENST00000399249.6 )
MYBPC3 p.Glu542Gln (p.E542Q) ( ENST00000399249.6, ENST00000545968.6 )
Associated Disease
Primary familial hypertrophic cardiomyopathy
Source Database
ClinVar
Description
NM_000256.3(MYBPC3):c.1624G>C (p.Glu542Gln) AND Primary familial hypertrophic cardiomyopathy
Observed Origin Sample
germline
ClinVar Allele ID
23647
ClinVar RefSeq Alternation Syntax
NM_000256.3:c.1624G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-10-27
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000035424
ClinVar Disease
Primary familial hypertrophic cardiomyopathy
Drugs