Annotation Detail

Information
Associated Genes
RNF213 RNF213-AS1
Associated Variants
RNF213 p.Arg4859Lys (p.R4859K) ( ENST00000582970.6, ENST00000508628.6 )
RNF213 p.Arg4859Lys (p.R4859K) ( ENST00000508628.6, ENST00000582970.6 )
Associated Disease
Moyamoya disease 2
Source Database
ClinVar
Description
NM_001256071.3(RNF213):c.14429G>A (p.Arg4810Lys) AND Moyamoya disease 2
ClinVar Allele ID
48299
ClinVar RefSeq Alternation Syntax
NM_001256071.3:c.14429G>A
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2022-07-26
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000032902
ClinVar Disease
Moyamoya disease 2
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
22931863
Pubmed
21048783
Pubmed
27515544
Pubmed
22377813
Pubmed
21799892
Drugs