Annotation Detail

Information
Associated Genes
GALT
Associated Variants
GALT p.Leu218= (p.L218=) ( ENST00000378842.8, ENST00000450095.6 )
GALT p.Leu218= (p.L218=) ( ENST00000378842.8, ENST00000450095.6 )
Associated Disease
Deficiency of UDPglucose-hexose-1-phosphate uridylyltransferase
Source Database
ClinVar
Description
NM_000155.4(GALT):c.652C>T (p.Leu218=) AND Deficiency of UDPglucose-hexose-1-phosphate uridylyltransferase
ClinVar Allele ID
18659
ClinVar RefSeq Alternation Syntax
NM_001258332.2:c.325C>T
ClinVar RefSeq Alternation Syntax
NM_000155.4:c.652C>T
Clinical Significance Description
Benign
Clinical Significance Last Update
2024-02-01
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000032587
ClinVar Disease
Deficiency of UDPglucose-hexose-1-phosphate uridylyltransferase
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs