Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB p.Ala955Val (p.A955V) ( ENST00000299314.12 )
GNPTAB p.Lys928Arg (p.K928R) ( ENST00000299314.12 )
GNPTAB p.Ala955Val (p.A955V) ( ENST00000299314.12 )
GNPTAB p.Lys928Arg (p.K928R) ( ENST00000299314.12 )
Associated Disease
Mucolipidosis type II
Source Database
ClinVar
Description
NM_024312.4(GNPTAB):c.[2783A>G;2864C>T]] AND Mucolipidosis type II
ClinVar Allele ID
47696
ClinVar Allele ID
47697
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.2864C>T
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.2783A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2012-05-10
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000032360
ClinVar Disease
Mucolipidosis type II
Observed Origin Sample
not provided
Drugs