Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB c.3335+6T>G ( ENST00000299314.12 )
GNPTAB c.3335+6T>G ( ENST00000299314.12 )
Associated Disease
Mucolipidosis type II
Source Database
ClinVar
Description
NM_024312.5(GNPTAB):c.3335+6T>G AND Mucolipidosis type II
ClinVar Allele ID
17812
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.3335+6T>G
Clinical Significance Description
Pathogenic
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000032336
ClinVar Disease
Mucolipidosis type II
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs