Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB p.Tyr56Ter (p.Y56*) ( ENST00000549165.1, ENST00000392919.4, ENST00000299314.12, ENST00000549940.5 )
GNPTAB p.Tyr56Ter (p.Y56*) ( ENST00000299314.12, ENST00000392919.4, ENST00000549165.1, ENST00000549940.5 )
Associated Disease
Pseudo-Hurler polydystrophy
Source Database
ClinVar
Description
NM_024312.5(GNPTAB):c.168T>A (p.Tyr56Ter) AND Pseudo-Hurler polydystrophy
ClinVar Allele ID
47641
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.168T>A
Clinical Significance Description
not provided
Clinical Significance Review Status
no assertion provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000032303
ClinVar Disease
Pseudo-Hurler polydystrophy
Observed Origin Sample
unknown
Drugs