Annotation Detail

Information
Associated Genes
SLC2A1
Associated Variants
SLC2A1 p.Arg93Trp (p.R93W) ( ENST00000426263.10, ENST00000674765.1 )
SLC2A1 p.Arg93Trp (p.R93W) ( ENST00000426263.10, ENST00000674765.1 )
Associated Disease
Childhood onset GLUT1 deficiency syndrome 2
Source Database
ClinVar
Description
NM_006516.4(SLC2A1):c.277C>T (p.Arg93Trp) AND Childhood onset GLUT1 deficiency syndrome 2
ClinVar Allele ID
31156
ClinVar RefSeq Alternation Syntax
NM_006516.4:c.277C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2009-12-08
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000030922
ClinVar Disease
Childhood onset GLUT1 deficiency syndrome 2
Observed Origin Sample
germline
Pubmed
19996082
Pubmed
18403583
Drugs