Annotation Detail

Information
Associated Genes
TERT
Associated Variants
TERT p.Lys902Arg (p.K902R) ( ENST00000310581.10, ENST00000334602.10 )
TERT p.Lys902Arg (p.K902R) ( ENST00000310581.10, ENST00000334602.10 )
Associated Disease
Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1
Source Database
ClinVar
Description
NM_198253.3(TERT):c.2705A>G (p.Lys902Arg) AND Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1
ClinVar Allele ID
45607
ClinVar RefSeq Alternation Syntax
NM_198253.3:c.2705A>G
ClinVar RefSeq Alternation Syntax
NM_001193376.3:c.2654+1922A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2011-05-26
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000030630
ClinVar Disease
Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1
Observed Origin Sample
germline
Pubmed
21436073
Drugs