Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Ala276Gly (p.A276G) ( ENST00000541395.5, ENST00000400024.6, ENST00000257555.11, ENST00000544413.2 )
HNF1A p.Ala276Gly (p.A276G) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
maturity-onset diabetes of the young type 3
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.827C>G (p.Ala276Gly) AND Maturity-onset diabetes of the young type 3
ClinVar Allele ID
45493
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.827C>G
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.827C>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2023-01-06
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000030513
ClinVar Disease
Maturity-onset diabetes of the young type 3
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs