Annotation Detail

Information
Associated Genes
SPINK1
Associated Variants
SPINK1 p.Ser10ValfsTer6 (p.S10Vfs*6) ( ENST00000296695.10, ENST00000510027.2 )
SPINK1 p.Ser10ValfsTer6 (p.S10Vfs*6) ( ENST00000296695.10, ENST00000510027.2 )
Associated Disease
Hereditary pancreatitis
Source Database
ClinVar
Description
NM_001379610.1(SPINK1):c.27del (p.Ser10fs) AND Hereditary pancreatitis
ClinVar Allele ID
45441
ClinVar RefSeq Alternation Syntax
NM_003122.5:c.27del
ClinVar RefSeq Alternation Syntax
NM_001379610.1:c.27del
ClinVar RefSeq Alternation Syntax
NM_001354966.2:c.27del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2024-01-10
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000030460
ClinVar Disease
Hereditary pancreatitis
Observed Origin Sample
germline
Drugs