Annotation Detail

Information
Associated Genes
HBB LOC107133510 LOC110006319
Associated Variants
HBB p.Glu122Gln (p.E122Q) ( ENST00000335295.4, ENST00000647020.1 )
HBB p.Glu122Gln (p.E122Q) ( ENST00000335295.4, ENST00000647020.1 )
Associated Disease
beta thalassemia
Source Database
ClinVar
Description
NM_000518.4(HBB):c.364G>C (p.Glu122Gln) AND beta Thalassemia
ClinVar Allele ID
30191
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.364G>C
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2022-11-03
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000029994
ClinVar Disease
beta Thalassemia
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs