Annotation Detail

Information
Associated Genes
PIK3CA
Associated Variants
PIK3CA p.His1047Arg (p.H1047R) ( ENST00000263967.4, ENST00000643187.1 )
PIK3CA p.His1047Arg (p.H1047R) ( ENST00000263967.4, ENST00000643187.1 )
Associated Disease
CLOVES syndrome
Source Database
ClinVar
Description
NM_006218.4(PIK3CA):c.3140A>G (p.His1047Arg) AND CLOVES syndrome
ClinVar Allele ID
28691
ClinVar RefSeq Alternation Syntax
NM_006218.4:c.3140A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-11-11
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000024621
ClinVar Disease
CLOVES syndrome
Observed Origin Sample
germline
Observed Origin Sample
de novo
Observed Origin Sample
somatic
Observed Origin Sample
unknown
Pubmed
22658544
Pubmed
17673550
Pubmed
15608678
Pubmed
26266975
Pubmed
23100325
Pubmed
34496175
Pubmed
26266985
Pubmed
22729222
Pubmed
15016963
Pubmed
15520168
Drugs