Annotation Detail

Information
Associated Genes
ACTG1
Associated Variants
ACTG1 p.Thr203Lys (p.T203K) ( ENST00000575842.5, ENST00000571691.6, ENST00000575994.6, ENST00000571721.6, ENST00000644774.2, ENST00000573283.7, ENST00000681052.1, ENST00000575087.5, ENST00000679480.1, ENST00000570382.2, ENST00000615544.5, ENST00000575659.6 )
ACTG1 p.Thr203Lys (p.T203K) ( ENST00000570382.2, ENST00000571691.6, ENST00000571721.6, ENST00000573283.7, ENST00000575087.5, ENST00000575659.6, ENST00000575842.5, ENST00000575994.6, ENST00000615544.5, ENST00000644774.2, ENST00000679480.1, ENST00000681052.1 )
Associated Disease
Baraitser-Winter syndrome 2
Source Database
ClinVar
Description
NM_001614.5(ACTG1):c.608C>A (p.Thr203Lys) AND Baraitser-winter syndrome 2
ClinVar Allele ID
38542
ClinVar RefSeq Alternation Syntax
NM_001199954.3:c.608C>A
ClinVar RefSeq Alternation Syntax
NM_001614.5:c.608C>A
ClinVar RefSeq Alternation Syntax
NR_037688.3:n.680C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2012-02-26
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000022425
ClinVar Disease
Baraitser-winter syndrome 2
Observed Origin Sample
germline
Pubmed
22366783
Drugs