Annotation Detail

Information
Associated Genes
TFR2
Associated Variants
TFR2 p.Arg105Ter (p.R105*) ( ENST00000223051.8, ENST00000431692.5, ENST00000462107.1 )
TFR2 p.Arg105Ter (p.R105*) ( ENST00000223051.8, ENST00000431692.5, ENST00000462107.1 )
Associated Disease
hemochromatosis type 3
Source Database
ClinVar
Description
NM_003227.4(TFR2):c.313C>T (p.Arg105Ter) AND Hemochromatosis type 3
ClinVar Allele ID
34227
ClinVar RefSeq Alternation Syntax
NM_003227.4:c.313C>T
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2023-08-13
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000020548
ClinVar Disease
Hemochromatosis type 3
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs