Annotation Detail

Information
Associated Genes
KCNJ11
Associated Variants
KCNJ11 p.Phe35Val (p.F35V) ( ENST00000682350.1, ENST00000682764.1, ENST00000339994.5, ENST00000528731.1 )
KCNJ11 p.Phe35Val (p.F35V) ( ENST00000339994.5, ENST00000528731.1, ENST00000682350.1, ENST00000682764.1 )
Associated Disease
permanent neonatal diabetes mellitus
Source Database
ClinVar
Description
NM_000525.4(KCNJ11):c.103T>G (p.Phe35Val) AND Permanent neonatal diabetes mellitus
ClinVar Allele ID
34047
ClinVar RefSeq Alternation Syntax
NM_000525.4:c.103T>G
ClinVar RefSeq Alternation Syntax
NM_001377296.1:c.-17+29T>G
ClinVar RefSeq Alternation Syntax
NM_001166290.2:c.-16-143T>G
ClinVar RefSeq Alternation Syntax
NM_001377297.1:c.-16-143T>G
Clinical Significance Description
not provided
Clinical Significance Review Status
no assertion provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000020346
ClinVar Disease
Permanent neonatal diabetes mellitus
Observed Origin Sample
unknown
Drugs