Annotation Detail

Information
Associated Genes
INS INS-IGF2
Associated Variants
INS p.Tyr108Cys (p.Y108C), INS-IGF2 c.187+923A>G ( ENST00000250971.7, ENST00000397270.1, ENST00000381330.5, ENST00000397262.5, ENST00000512523.1 )
INS p.Tyr108Cys (p.Y108C), INS-IGF2 c.187+923A>G ( ENST00000250971.7, ENST00000381330.5, ENST00000397262.5, ENST00000512523.1, ENST00000397270.1 )
Associated Disease
permanent neonatal diabetes mellitus
Source Database
ClinVar
Description
NM_000207.3(INS):c.323A>G (p.Tyr108Cys) AND Permanent neonatal diabetes mellitus
ClinVar Allele ID
33972
ClinVar RefSeq Alternation Syntax
NM_001042376.3:c.187+923A>G
ClinVar RefSeq Alternation Syntax
NM_001291897.2:c.323A>G
ClinVar RefSeq Alternation Syntax
NM_000207.3:c.323A>G
ClinVar RefSeq Alternation Syntax
NM_001185098.2:c.323A>G
ClinVar RefSeq Alternation Syntax
NM_001185097.2:c.323A>G
Clinical Significance Description
not provided
Clinical Significance Review Status
no assertion provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000020210
ClinVar Disease
Permanent neonatal diabetes mellitus
Observed Origin Sample
not provided
Observed Origin Sample
unknown
Drugs