Annotation Detail

Information
Associated Genes
APOE
Associated Variants
APOE p.Arg176Cys (p.R176C) ( ENST00000252486.9 )
APOE p.Val254Glu (p.V254E) ( ENST00000252486.9 )
APOE p.Arg176Cys (p.R176C) ( ENST00000252486.9 )
APOE p.Val254Glu (p.V254E) ( ENST00000252486.9 )
Associated Disease
Familial type 3 hyperlipoproteinemia
Source Database
ClinVar
Description
NM_000041.3(APOE):c.[526C>T;761T>A] AND Familial type 3 hyperlipoproteinemia
ClinVar Allele ID
32887
ClinVar Allele ID
38491
ClinVar RefSeq Alternation Syntax
NM_001302690.2:c.761T>A
ClinVar RefSeq Alternation Syntax
NM_001302689.2:c.526C>T
ClinVar RefSeq Alternation Syntax
NM_001302690.2:c.526C>T
ClinVar RefSeq Alternation Syntax
NM_001302691.2:c.526C>T
ClinVar RefSeq Alternation Syntax
NM_000041.4:c.761T>A
ClinVar RefSeq Alternation Syntax
NM_001302689.2:c.761T>A
ClinVar RefSeq Alternation Syntax
NM_000041.4:c.526C>T
ClinVar RefSeq Alternation Syntax
NM_001302691.2:c.761T>A
ClinVar RefSeq Alternation Syntax
NM_001302688.2:c.604C>T
ClinVar RefSeq Alternation Syntax
NM_001302688.2:c.839T>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1993-05-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000019454
ClinVar Disease
Familial type 3 hyperlipoproteinemia
Observed Origin Sample
germline
Pubmed
8488843
Drugs