Annotation Detail

Information
Associated Genes
COL7A1
Associated Variants
COL7A1 p.Arg2063Trp (p.R2063W) ( ENST00000328333.12, ENST00000681320.1 )
COL7A1 p.Arg2063Trp (p.R2063W) ( ENST00000328333.12, ENST00000681320.1 )
Associated Disease
recessive dystrophic epidermolysis bullosa
Source Database
ClinVar
Description
NM_000094.4(COL7A1):c.6187C>T (p.Arg2063Trp) AND Recessive dystrophic epidermolysis bullosa
ClinVar Allele ID
32495
ClinVar RefSeq Alternation Syntax
NM_000094.4:c.6187C>T
Clinical Significance Description
Pathogenic
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000019007
ClinVar Disease
Recessive dystrophic epidermolysis bullosa
Observed Origin Sample
germline
Pubmed
18030675
Pubmed
9326325
Drugs