Annotation Detail

Information
Associated Genes
COL7A1
Associated Variants
COL7A1 p.Gly2034Arg (p.G2034R) ( ENST00000328333.12, ENST00000681320.1 )
COL7A1 p.Gly2034Arg (p.G2034R) ( ENST00000328333.12, ENST00000681320.1 )
Associated Disease
Generalized dominant dystrophic epidermolysis bullosa
Source Database
ClinVar
Description
NM_000094.4(COL7A1):c.6100G>A (p.Gly2034Arg) AND Generalized dominant dystrophic epidermolysis bullosa
ClinVar Allele ID
32489
ClinVar RefSeq Alternation Syntax
NM_000094.4:c.6100G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2002-03-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000019001
ClinVar Disease
Generalized dominant dystrophic epidermolysis bullosa
Observed Origin Sample
germline
Pubmed
8345225
Pubmed
10084325
Pubmed
11874498
Pubmed
9347800
Pubmed
9856844
Drugs