Annotation Detail

Information
Associated Genes
COL2A1
Associated Variants
COL2A1 p.Arg653Ter (p.R653*) ( ENST00000337299.7, ENST00000380518.8 )
COL2A1 p.Arg653Ter (p.R653*) ( ENST00000337299.7, ENST00000380518.8 )
Associated Disease
Stickler syndrome type 1
Source Database
ClinVar
Description
NM_001844.5(COL2A1):c.1957C>T (p.Arg653Ter) AND Stickler syndrome type 1
ClinVar Allele ID
32434
ClinVar RefSeq Alternation Syntax
NM_001844.5:c.1957C>T
ClinVar RefSeq Alternation Syntax
NM_033150.3:c.1750C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-11-10
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000018938
ClinVar Disease
Stickler syndrome type 1
Observed Origin Sample
germline
Pubmed
12939326
Pubmed
10982970
Drugs