Annotation Detail

Information
Associated Genes
COL2A1
Associated Variants
COL2A1 p.Leu667Phe (p.L667F) ( ENST00000337299.7, ENST00000380518.8 )
COL2A1 p.Leu667Phe (p.L667F) ( ENST00000337299.7, ENST00000380518.8 )
Associated Disease
Stickler syndrome, type I, nonsyndromic ocular
Source Database
ClinVar
Description
NM_001844.5(COL2A1):c.1999C>T (p.Leu667Phe) AND Stickler syndrome, type I, nonsyndromic ocular
ClinVar Allele ID
32423
ClinVar RefSeq Alternation Syntax
NM_033150.3:c.1792C>T
ClinVar RefSeq Alternation Syntax
NM_001844.5:c.1999C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2005-02-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000018927
ClinVar Disease
Stickler syndrome, type I, nonsyndromic ocular
Observed Origin Sample
germline
Pubmed
15671297
Pubmed
11007540
Drugs