Annotation Detail

Information
Associated Genes
CFH
Associated Variants
ENSG00000289697 p.Gln408Ter (p.Q408*), CFH p.Gln408Ter (p.Q408*) ( ENST00000695968.1, ENST00000696030.1, ENST00000696028.1, ENST00000695978.1, ENST00000695987.1, ENST00000630130.2, ENST00000696023.1, ENST00000696029.1, ENST00000696027.1, ENST00000695981.1, ENST00000695984.1, ENST00000359637.3, ENST00000695970.1, ENST00000367429.9, ENST00000695976.1, ENST00000695979.1, ENST00000695974.1, ENST00000695969.1, ENST00000695971.1 )
ENSG00000289697 p.Gln408Ter (p.Q408*), CFH p.Gln408Ter (p.Q408*) ( ENST00000359637.3, ENST00000367429.9, ENST00000630130.2, ENST00000695968.1, ENST00000695969.1, ENST00000695970.1, ENST00000695971.1, ENST00000695974.1, ENST00000695976.1, ENST00000695978.1, ENST00000695979.1, ENST00000695981.1, ENST00000695984.1, ENST00000695987.1, ENST00000696023.1, ENST00000696027.1, ENST00000696028.1, ENST00000696029.1, ENST00000696030.1 )
Associated Disease
basal laminar drusen
Source Database
ClinVar
Description
NM_000186.4(CFH):c.1222C>T (p.Gln408Ter) AND Basal laminar drusen
ClinVar Allele ID
31599
ClinVar RefSeq Alternation Syntax
NM_000186.4:c.1222C>T
ClinVar RefSeq Alternation Syntax
NM_001014975.3:c.1222C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2008-02-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000018028
ClinVar Disease
Basal laminar drusen
Observed Origin Sample
germline
Pubmed
18252232
Drugs