Annotation Detail

Information
Associated Genes
FGFR3
Associated Variants
FGFR3 p.Lys652Asn (p.K652N) ( ENST00000340107.9, ENST00000352904.6, ENST00000412135.7, ENST00000440486.8, ENST00000481110.7 )
FGFR3 p.Lys652Asn (p.K652N) ( ENST00000340107.9, ENST00000352904.6, ENST00000412135.7, ENST00000440486.8, ENST00000481110.7 )
Associated Disease
hypochondroplasia
Source Database
ClinVar
Description
NM_000142.5(FGFR3):c.1950G>C (p.Lys650Asn) AND Hypochondroplasia
ClinVar Allele ID
31386
ClinVar RefSeq Alternation Syntax
NM_001354809.2:c.1953G>C
ClinVar RefSeq Alternation Syntax
NR_148971.2:n.2376G>C
ClinVar RefSeq Alternation Syntax
NM_022965.4:c.1614G>C
ClinVar RefSeq Alternation Syntax
NM_000142.5:c.1950G>C
ClinVar RefSeq Alternation Syntax
NM_001163213.2:c.1956G>C
ClinVar RefSeq Alternation Syntax
NM_001354810.2:c.1953G>C
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2021-06-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000017756
ClinVar Disease
Hypochondroplasia
Observed Origin Sample
germline
Observed Origin Sample
paternal
Pubmed
11055896
Drugs