Annotation Detail

Information
Associated Genes
FUS
Associated Variants
FUS p.Arg524Trp (p.R524W) ( ENST00000568685.1, ENST00000380244.8, ENST00000715542.1, ENST00000254108.12 )
FUS p.Arg524Trp (p.R524W) ( ENST00000254108.12, ENST00000380244.8, ENST00000568685.1, ENST00000715542.1 )
Associated Disease
amyotrophic lateral sclerosis type 6
Source Database
ClinVar
Description
NM_004960.4(FUS):c.1570A>T (p.Arg524Trp) AND Amyotrophic lateral sclerosis type 6
ClinVar Allele ID
31267
ClinVar RefSeq Alternation Syntax
NM_001170937.1:c.1558A>T
ClinVar RefSeq Alternation Syntax
NM_001170634.1:c.1567A>T
ClinVar RefSeq Alternation Syntax
NM_004960.4:c.1570A>T
ClinVar RefSeq Alternation Syntax
NR_028388.2:n.1640A>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2010-04-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000017615
ClinVar Disease
Amyotrophic lateral sclerosis type 6
Observed Origin Sample
germline
Pubmed
20385912
Drugs