Annotation Detail

Information
Associated Genes
HBB LOC107133510 LOC110006319
Associated Variants
HBB p.Ala116Asp (p.A116D) ( ENST00000335295.4, ENST00000647020.1 )
HBB p.Ala116Asp (p.A116D) ( ENST00000335295.4, ENST00000647020.1 )
Associated Disease
hemoglobinopathy
Source Database
ClinVar
Description
NM_000518.5(HBB):c.347C>A (p.Ala116Asp) AND Hemoglobinopathy
ClinVar Allele ID
30565
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.347C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1993-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016791
ClinVar Disease
Hemoglobinopathy
Observed Origin Sample
germline
Pubmed
7693620
Drugs