Annotation Detail

Information
Associated Genes
HBB LOC106099062 LOC107133510
Associated Variants
HBB p.? (p.?) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
HBB p.? (p.?) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
Associated Disease
Beta zero thalassemia
Source Database
ClinVar
Description
NM_000518.5(HBB):c.3G>A (p.Met1Ile) AND Beta zero thalassemia
Pubmed
8330972
ClinVar Allele ID
30558
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.3G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1993-06-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016783
ClinVar Disease
Beta zero thalassemia
Observed Origin Sample
germline
Pubmed
1301952
Drugs