Annotation Detail

Information
Associated Genes
HBB LOC106099062 LOC107133510
Associated Variants
HBB p.His93Asn (p.H93N) ( ENST00000647020.1, ENST00000335295.4, ENST00000485743.1 )
HBB p.His93Asn (p.H93N) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
Associated Disease
hemoglobinopathy
Source Database
ClinVar
Description
NM_000518.4(HBB):c.277C>A (p.His93Asn) AND Hemoglobinopathy
ClinVar Allele ID
30533
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.277C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-12-12
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016756
ClinVar Disease
Hemoglobinopathy
Observed Origin Sample
germline
Pubmed
1951318
Pubmed
1787097
Drugs