Annotation Detail

Information
Associated Genes
HBB LOC107133510 LOC110006319
Associated Variants
HBB p.Val110CysfsTer49 (p.V110Cfs*49) ( ENST00000647020.1, ENST00000335295.4 )
HBB p.Val110CysfsTer49 (p.V110Cfs*49) ( ENST00000335295.4, ENST00000647020.1 )
Associated Disease
Beta zero thalassemia
Source Database
ClinVar
Description
NM_000518.5(HBB):c.328del (p.Val110fs) AND Beta zero thalassemia
ClinVar Allele ID
30469
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.328del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1986-06-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016687
ClinVar Disease
Beta zero thalassemia
Observed Origin Sample
germline
Pubmed
3014870
Drugs