Annotation Detail

Information
Associated Genes
HBB LOC107133510 LOC110006319
Associated Variants
HBB p.Leu115GlyfsTer44 (p.L115Gfs*44) ( ENST00000335295.4, ENST00000647020.1 )
HBB p.Leu115GlyfsTer44 (p.L115Gfs*44) ( ENST00000335295.4, ENST00000647020.1 )
Associated Disease
Beta zero thalassemia
Source Database
ClinVar
Description
NM_000518.5(HBB):c.343_344delinsG (p.Leu115fs) AND Beta zero thalassemia
ClinVar Allele ID
30464
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.343_344delinsG
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1988-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016681
ClinVar Disease
Beta zero thalassemia
Observed Origin Sample
germline
Pubmed
3401599
Drugs