Annotation Detail

Information
Associated Genes
HBB LOC106099062 LOC107133510
Associated Variants
HBB p.Lys9ValfsTer14 (p.K9Vfs*14) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
HBB p.Lys9ValfsTer14 (p.K9Vfs*14) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
Associated Disease
Beta zero thalassemia
Source Database
ClinVar
Description
NM_000518.5(HBB):c.25_26del (p.Lys9fs) AND Beta zero thalassemia
ClinVar Allele ID
30452
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.25_26del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1995-04-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016669
ClinVar Disease
Beta zero thalassemia
Observed Origin Sample
germline
Pubmed
7795641
Pubmed
6985481
Drugs