Annotation Detail

Information
Associated Genes
HBB LOC106099062 LOC107133510
Associated Variants
HBB p.Lys83? (p.K83?) ( ENST00000485743.1, ENST00000335295.4, ENST00000647020.1 )
HBB p.Glu7Val (p.E7V) ( ENST00000647020.1, ENST00000485743.1, ENST00000335295.4 )
HBB p.Lys83? (p.K83?) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
HBB p.Glu7Val (p.E7V) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
Associated Disease
HEMOGLOBIN S (PROVIDENCE)
Source Database
ClinVar
Description
NM_000518.4(HBB):c.[20A>T;249G>Y] AND HEMOGLOBIN S (PROVIDENCE)
ClinVar Allele ID
30372
ClinVar Allele ID
30358
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.249G>Y
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.20A>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1988-10-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016579
ClinVar Disease
HEMOGLOBIN S (PROVIDENCE)
Observed Origin Sample
germline
Pubmed
3191036
Drugs