Annotation Detail

Information
Associated Genes
HBB LOC107133510 LOC110006319
Associated Variants
HBB p.Val135Glu (p.V135E) ( ENST00000335295.4, ENST00000647020.1 )
HBB p.Val135Glu (p.V135E) ( ENST00000335295.4, ENST00000647020.1 )
Associated Disease
hemoglobinopathy
Source Database
ClinVar
Description
NM_000518.5(HBB):c.404T>A (p.Val135Glu) AND Hemoglobinopathy
ClinVar Allele ID
30329
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.404T>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1987-01-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016521
ClinVar Disease
Hemoglobinopathy
Observed Origin Sample
germline
Pubmed
891976
Pubmed
3588028
Drugs