Annotation Detail

Information
Associated Genes
HBB LOC106099062 LOC107133510
Associated Variants
HBB p.Ala28Ser (p.A28S) ( ENST00000485743.1, ENST00000335295.4, ENST00000647020.1 )
HBB p.Ala28Ser (p.A28S) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
Associated Disease
Beta-plus-thalassemia
Source Database
ClinVar
Description
NM_000518.5(HBB):c.82G>T (p.Ala28Ser) AND Beta-plus-thalassemia
ClinVar Allele ID
30278
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.82G>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1989-01-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016440
ClinVar Disease
Beta-plus-thalassemia
Observed Origin Sample
germline
Pubmed
6469698
Pubmed
6668188
Pubmed
2467892
Pubmed
3114175
Pubmed
6733281
Pubmed
6664996
Drugs