Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Ser531Thr (p.S531T) ( ENST00000541395.5, ENST00000544413.2, ENST00000257555.11 )
HNF1A p.Ser531Thr (p.S531T) ( ENST00000257555.11, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
maturity-onset diabetes of the young type 3
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.1592G>C (p.Ser531Thr) AND Maturity-onset diabetes of the young type 3
ClinVar Allele ID
29986
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.1592G>C
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.1592G>C
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2017-04-27
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016085
ClinVar Disease
Maturity-onset diabetes of the young type 3
Observed Origin Sample
germline
Pubmed
12574234
Drugs