Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Pro112Leu (p.P112L) ( ENST00000541395.5, ENST00000400024.6, ENST00000257555.11, ENST00000544413.2 )
HNF1A p.Pro112Leu (p.P112L) ( ENST00000400024.6, ENST00000257555.11, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
maturity-onset diabetes of the young type 3
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.335C>T (p.Pro112Leu) AND Maturity-onset diabetes of the young type 3
ClinVar Allele ID
29981
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.335C>T
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.335C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-05-06
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016080
ClinVar Disease
Maturity-onset diabetes of the young type 3
Observed Origin Sample
germline
Pubmed
12574234
Pubmed
11162430
Pubmed
12107757
Drugs