Annotation Detail

Information
Associated Genes
HNF1A C12orf43
Associated Variants
HNF1A p.Thr627Ile (p.T627I) ( ENST00000544413.2, ENST00000288757.7, ENST00000257555.11, ENST00000541395.5 )
HNF1A p.Thr627Ile (p.T627I) ( ENST00000257555.11, ENST00000541395.5, ENST00000544413.2, ENST00000288757.7 )
Associated Disease
maturity-onset diabetes of the young type 3
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.1859C>T (p.Thr620Ile) AND Maturity-onset diabetes of the young type 3
ClinVar Allele ID
29974
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.1880C>T
ClinVar RefSeq Alternation Syntax
NM_001286191.2:c.*2998G>A
ClinVar RefSeq Alternation Syntax
NM_001286196.2:c.*2998G>A
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.1859C>T
ClinVar RefSeq Alternation Syntax
NM_022895.3:c.*2998G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1999-09-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016072
ClinVar Disease
Maturity-onset diabetes of the young type 3
Observed Origin Sample
germline
Pubmed
10482964
Drugs