Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Arg272His (p.R272H) ( ENST00000400024.6, ENST00000257555.11, ENST00000541395.5, ENST00000544413.2 )
HNF1A p.Arg272His (p.R272H) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
type 1 diabetes mellitus 20
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.815G>A (p.Arg272His) AND Type 1 diabetes mellitus 20
ClinVar Allele ID
29970
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.815G>A
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.815G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1997-10-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016068
ClinVar Disease
Type 1 diabetes mellitus 20
Observed Origin Sample
germline
Pubmed
9313763
Drugs