Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Pro447Leu (p.P447L) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
HNF1A p.Pro447Leu (p.P447L) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
maturity-onset diabetes of the young type 3
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.1340C>T (p.Pro447Leu) AND Maturity-onset diabetes of the young type 3
ClinVar Allele ID
29967
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.1340C>T
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.1340C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1997-04-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000016065
ClinVar Disease
Maturity-onset diabetes of the young type 3
Observed Origin Sample
germline
Pubmed
9075819
Pubmed
8945470
Drugs