Annotation Detail

Information
Associated Genes
SOD1
Associated Variants
SOD1 p.Leu127Ter (p.L127*) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Leu127Ter (p.L127*) ( ENST00000270142.11, ENST00000389995.4 )
Associated Disease
amyotrophic lateral sclerosis type 1
Source Database
ClinVar
Description
NM_000454.5(SOD1):c.380T>A (p.Leu127Ter) AND Amyotrophic lateral sclerosis type 1
ClinVar Allele ID
29816
ClinVar RefSeq Alternation Syntax
NM_000454.5:c.380T>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1997-05-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000015900
ClinVar Disease
Amyotrophic lateral sclerosis type 1
Observed Origin Sample
germline
Pubmed
10735277
Drugs