Annotation Detail

Information
Associated Genes
LAMB3
Associated Variants
LAMB3 p.Trp302GlyfsTer94 (p.W302Gfs*94) ( ENST00000356082.9, ENST00000391911.5, ENST00000367030.7 )
LAMB3 p.Trp302GlyfsTer94 (p.W302Gfs*94) ( ENST00000356082.9, ENST00000367030.7, ENST00000391911.5 )
Associated Disease
Junctional epidermolysis bullosa, non-Herlitz type
Source Database
ClinVar
Description
NM_000228.3(LAMB3):c.904del (p.Trp302fs) AND Junctional epidermolysis bullosa, non-Herlitz type
ClinVar Allele ID
29581
ClinVar RefSeq Alternation Syntax
NM_001017402.2:c.904del
ClinVar RefSeq Alternation Syntax
NM_001127641.1:c.904del
ClinVar RefSeq Alternation Syntax
NM_000228.3:c.904del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2006-12-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000015643
ClinVar Disease
Junctional epidermolysis bullosa, non-Herlitz type
Observed Origin Sample
germline
Pubmed
9501007
Pubmed
17115047
Drugs