Annotation Detail

Information
Associated Genes
KCNH2
Associated Variants
KCNH2 p.Thr65Pro (p.T65P) ( ENST00000262186.10, ENST00000713710.1 )
KCNH2 p.Thr65Pro (p.T65P) ( ENST00000262186.10, ENST00000713710.1 )
Associated Disease
long QT syndrome 2
Source Database
ClinVar
Description
NM_000238.4(KCNH2):c.193A>C (p.Thr65Pro) AND Long QT syndrome 2
ClinVar Allele ID
29473
ClinVar RefSeq Alternation Syntax
NM_000238.4:c.193A>C
ClinVar RefSeq Alternation Syntax
NM_001406755.1:c.16A>C
ClinVar RefSeq Alternation Syntax
NM_172056.3:c.193A>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2002-12-13
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000015515
ClinVar Disease
Long QT syndrome 2
Observed Origin Sample
germline
Pubmed
12354768
Drugs